Saturday, 29 August 2020

Detailed viva on Club Foot

Findings

Small foot , stretched skin  on dorsolateral region and thrown into creases along medial aspect

scars and callosities

head of talus palpable

lateral convex border and medial concavity with furrows

heel rotated medially and drawn up

ancilliary

  genu valgum ,

  extrinsic  / intrinsic type

gait - stumbling

ROM -

  ankle , knee , inversion , eversion at subtalar joint

other examination

 hip for DDH

  Spine for Dysrahism

  Cerebral Palsy

  Polio - tight iliotibial band

    cleft lip , palate , exomphalos  and congenital hernia

correctible or not

Impression -

                   Primary or Idiopathic Secondary Clubfoot

                    Recurrent Club Foot

     


Deformities in club Foot

 equinus at ankle

 varus and internal rotation

 forefoot adduction and supination

midfoot cavus

others -

 internal rotation of tibia

 atrophy of claves and smaller circumference than others

 small foot

How do you look for equinus , varus , adduction ?

Heel varus from behind  the patients

Supination

    behind - 2 concave curves above and below lateral malleolus are normal #
 
                  if curve below lateral mallolus is convex outwoards suggest supinated foot


  Equinus oberved from side

Adduction of forefoot - observed from behind . Great toe prominently seen .


Cavus - - medial longitudinal arch , prominent on tip toeing

Supination - combination of the deformities


                  abduction of forefoot

                  internal rotation and plantar flexion at ankle

                  inversion at subtalar joint

                  medial arch elevation

                 
Pronation

                  forefoot abduction

                   hindfoot eversion

                   DF at ankle

                    depression at ankle


    Silfverskiold test
 Improved Dorsiflexion on flexing knee which suggests Gastrosoleus tightness .

             

Etilogy of CTEV

1.Intrauterine packaging defet - Primi , Oligohydraminous

2.Neuromuscular defect - Spina Bifida , AMC

3.Fetal Developmental arrest in fibular stage

4.Defective Cartilage enlage of talus

5.Retracting fibrosis

6.Anomalous tendon insertion

7. Germ plasm Defect

8.Myoblast in medial fascia

9.Hereditary ; polygenic multifactorial trait ; 1:35 chances if sibling affected ; 1 : 3 if twin affected
               
   deletion of chromosme 2 (2q3, : 33 ) related to CASP gene ( Heck et al. , Edwards   Syndrome )
       

10.Electromagnetic radiation and toxins ( paternal smoking , drugs )

11.Vascular thoery ;  Absent anterior tibial artery or posterior tibial artery in parents.

12.Infective Pathogens ; enteroviruses , conflicting evidence



Syndromes associated with CTEV

AMC

Streeter's Dysplasia

Tibial Hemimilia

Down's syndrome

Larsen Syndrome

Fetal Alcohol Syndrome

 Pierre - Robin Syndrome

 Opitz Syndrome

 Prunnel Belly Syndrome

  Freeman - Sheldon Syndrome (whistling fac )



Club Foot types

 Kawashima classification


Type 1

 Extrinsic / Non - rigid

foot normal sized  , mild varus

heel can be brought down with ease , minimal varus

creases normal

telescopy absent



Type II

 Intrinsic / Rigid

foot small , marked varus

heel cant be brought down with ease , marked varus

deep medial , posterior and plantar creases

telescopy present




Aims of treatment

supple plantigrade foot with good function


Objectives of correction

  to correct deformity early , fully and develop muscle power of limb sufficiently to maintain correction


Manipulation Techniques

  Kite and Lovells

          calcaneocuboid junction- fulcrum which prevented abduction of calcaneum and whole foot

           remains in adduction and forefoot relatively more .

   Ponseti's method of straping and taping for premature babies , babies with multiple anomalies and   

            baibes under treatment in ICU requiring multiple blood samples .


  Montepiller and Dimglio method of CPM

 Botox injection into Tendoachillies


Sequence of correctio of Club Foot

  C- lifting Ist MT and more supination

   A- Abduction

    V- it corrects itself

   E - heel cord release , last cast applied for 3 weeks


Ponseti Method of treatment .

      manipulative casting technique to simultaneously correct deformity from pronation to equinus in end.

concept - relaxation of collagen and atraumatic remodelling of joint surfaces - Talonavicular ,

Calcaneocuboid , Talocalcaneal.


What defines the end of treatment ?

1. no adduction / inversion deformity

2. hollow on dorusm of foot previously occupied by talar head

3. passive movement to full calcaneovalgus

4. child able to evert and dorsiflex foot voluntarily to about right angle

5. squat test



What is Spurious correction ?
apparent correction without actual correction or development of new unrelated deformities due to faulty manipulation

   Rocker bottom deformities

     Bean shaped foot

     Skewed foot

      fractures

     flat top talus



How do you manage ?

Take AP and lateral radiogarphs

Scoring of foot - Dimeligo scoring and classification

          AP -   talocalcaneal - 25 - 50 degrees normal

                                             less than 25 degrees - CTEV

            Lateral -  Talocalcaneal angle 25- 50 degrees

                                             less than 25 degrees in CTEV.


         Correction depends on Age and Rigidity of the deformity .

                           choices ; Ponseti Method , Ilizarov , Triple Arthrodesis , Posteromedial release

   
  Early presentation ,Pirani scoring is useful.

 0- normal , 0- 5 moderately abnormal  ,  1 - severly abnormal



Midfoot score

           0- 3
                      1. curved latereal border

                       2. medial crease

                       3. talar head coverage

   Hindfoot score

          0 - 3

                         1. posterior crease

                         2. rigid equinus

                          3. empty heel


Tenotomy done when hindfoot score > 1 AND midfoot score < 1 and head of talus fully covered.

treat as above and plot score on graph.



Soft tissue releases on clubfoot

 Indications ; neglected clubfoot ( < 4 years ) ,

                      resistant clubfoot or deformity

                       relapsed/residua deformity


 Ponseti applied to decrease magnitude of surgery ; various releases desribed

 1.Posterior releases

  2. Posteromedial release

 3. Extensile Posteromedial release

  4.Combined posteromedial and posterolateral release

  5. complete subtalar release

 timing is an issue

  French - within  few weeks to months capitalizing on remodelling potential of growing foot .

 Turco -     considers 1-2 years adequate timing as anatomic details become clearer , under/over

                 correction wont be magnified as foot grows if delayed.


Simon's - considers 8 cm foot size as approprite timing for release and not the age.



Different techniques for release are


Turco
   
           one stage Posteromedial release

Carol

           emphazied PMR + plantar fascia release + calcaneocuboid joint osteotomy as forefoot

             adduction and supination not addressed by Turco


Goldner

           Emphasized on correction of talar rotation by tibiotalar joint release leaving subtalr joint to

           prevent valgus overcorrection .


McKay and Simons - complete subtalar release which is actually a peritalar release with release of

                                   interosseous ligament and talonavicular joint and calcaneocuboid joint


                                  Posterior release only for persistent equinus , fully PM plantar and lateral

                                  release if all defomities persistent.



What structures are released in posteromedial soft tissue release of McKay ?

Incisions

     Turco - Hockeystick posteromedial release

      Cincinnati - Circumferential

      Caroll's and incision technique - posteromedial and a sall lateral


Medial release

      1. posterior and medial subtalar joint capsule ( preserve interosseous ligament )

      2. talonavicular joint capsule

       3. spring ligament

       4.Y - ligament

       5. Medial calcanecuboid capsule

       6. knot of henry

        7.abductor hallucis

         8.lengthening of posterior tibial tendon , FHL , FDL

         9 . Plantar fascia , quadratus plantae


 Posterior Release

         1. Ankle joint capsule

         2. subtalar joint capsule

         3.achillies tendon lengthening

          4. posterior talofibular ligament



Lateral Release

1. Lateral subtalar joint capsule

2. Peroneal tendon sheath

3. calcaneofibular ligament

4. lateral talocalcaneal ligament

5. ED Brevis, Calcaneocuboid ligament, Inferior Extensor Retinaculum , Calcaneonavicular ligament     
        in resistant cases .



Structures preserved

dorsal strucutres , medial neurovascular bundle , deltoid ligament , interosseous ligament

talonavicular joint subtalar joint often fixed with smooth K - wires.



Complications  of surgery

1.Neurovascular damage , physeal/ bony damage

2.Undercorrection - inadequate postoperative maintenance  (CAVE )

3. Overcorrection

            valgus , abduction  , calcaneous deformity , Pes Planus

4. Talar AVN

5. Sinus Tarsai syndrome

6. Dorsal Navicular subluxation leading to cavovarus foot

    Treatment - repeated plantar release + Tendoachillies lengthening

7. Skew foot

8. Dorsal bunion

   weak peroneus longus + strong DF and PF

         Treatment - Ist ray realignment + drosal FHB transfer with MTP release


Some terms

Neglected Clubfoot
 
                          Patient not getting any treatment upto 9 months of age .


Recurrent Clubfoot
       
                          1 or more deformity recurring during the course of treatment


Relapsed - 1 or more defromity which recur after sucessful treatment.
         
                       

Resistant Clubfoot

                        better termed persistent clubfoot

                         correction not obtained by manipulation / surgical methods (conservative /surgery ) 

                         in any or all of deformities


Role of tendon transfer in clubfoot

                          Evertor insufficiency - leads to Dynamic supination /inversion , weight borne on 

                                                               lateral aspect of foot

                       
                                             Tr.  -       Anterior Tibialis Tendon transfer

                                                          min. age  5 years

                                                       SPLATT (Split Anterior Tibialis Tendon Trasfer )
                                                         
                                                       tendon rerouted under retinaculum to cuboid /lateral cuneiforom


Triceps Surae  insufficiency - Calcaneous gait

 Prevention - overlengthening of Tendoachillies

 Option - Peronei , TP or long toe flexor

   Peroneus Brevis split and rerouted into calcaneal tuberosity with tenodesis of distal stump to longus to prevent evertor insufficiency



Bony Surgery in Clubfoot


Deformity

Metatarsus Adductus

                                   age > 5 years

                                                             Metatarsal osteotomy


Hindfoot Varus

                               < 2-3 years

                                                        Modified Mc Kay

                           3-10 years

                                                        Dwyer Osteotomy  (Heel Varus, lateral closing wedge osteotomy)

                                                        Dilwin Evans (Calcaneocuboid fuse, for long lat. column)

                                                        Lichtblau - Pseudoarthrosis (long lat. column)


                          10-12 years       

                                                       Triple Arthrodesis



 Equinus   

                                                      Posterior release (mild moderate deformity )

                                                      Lamrudini (severe )

                                                      Excision of portion of talar head /navicle

                                                      Distal tibial DF osteotomy (salvage )


Cavus     

                                    > 6 Years
                         
                                                    Japas V -Osteotomy

                                                     Akron mid-tarsal osteotomy (dome )

                                                     transmid tarsal


All deformities

                                     > 10 Years

                                                  triple arthrodesis


Persistent Intoeing gait

                                   > 2 years following correction

        a. tibial intorsion

        b. medial spin of hindfoot in ankle mortise

                                                                        supramalleoloar derotation osteotomy proximal to

                                                                       distal  tibia physis correcting 35 degree ER .


Medial deviation of forefoot due to talar neck deviation

                                                                                    Evans/ Lichtblau



Neglected Clubfoot or secondary clubfoot

                                                    adults                                       Cuneiform tarsectomy



                                               myelomeningocele                        talectomy
 
                                               severe resistant clubfoot

                     
                                               Neglected clubfoot                    wedge tarsectomy
                                                8-11 yers , hardly ever done



Methods of Surgery

Soft tissue release

Bony procedures

Ilizarov method

 simultanous 3 d multilevel correction

  correction without shortening of foot


Characteristics of club foot shoes (Robert Jones shoes )

1. straight inner border

2. outer shoe raise

3. no heel

maintain correction prevent relapse

also correct mild residual deformity in flexible foot.



DB Splint (Dennis Browne )

aka Abduction bar

consists of metal or Polypropylene Bar

                     shoes attached to ends over foot plate (Aluminium) rotated outwards at midline


shoes

  open toe high top with straight medial border

  velcro straps



 problems

       wight , pressure  sore , injury to infants and parents.


Classification ; Demeglio

  Gr                                                      Type                             Score

I                                                Benign                                     <5

II                                              Moderate                                   5- <10

III                                              Severe                                   10- <15


IV                                             Very severe                             15- < 20



Points ; 0-4

                                            Deformity                                             Points                                           

Supination                           < 20- 0                                                  1

Adduction                             0-    20                                                 2


Varus                                      20-45                                                 3

Equinus                                  45-90                                                  4




other parameters


poor muscle condition                           1

cavus                                                      1

Posterior crease                                    1

Medial Crease                                      1


Bracing Protocol

Abducted to 60 - 70 degrees (thigh foot axis )

unilateral ; 60- 70 degrees external rotation on clubfoot side , 30-40 degrees on normal side

B/L - 70 degrees ER on each side ,

Bar width equal to baby's shoulder width.

narrow bar - cause of lack of compliance

convexity 5- 10 degrees away from baby to hold foot in Dorsiflexion


Timing

 full time for first 3 months

 16 hours for 3-4 years

(12 hours night , day 4 hours )


During brace

 not child may develop eternal tibial torsion + heel valgus

 then decrease External rotation on shoe bar from 70 to 40 degrees.



Pirani score importance


assesss severity of club foot ,

monitor patients progress

predicts treatment outcomes

higher score - increases number of relapse in bracing phase




Ideal foot after triple arthrodesis

looks natural in shoes

no external rotation on foot - standing / walking

no need for brace

appears natural when bare

weight evenly distributes over plantar surface of foot

axis of ankle perpendicular to foot

no pain

pateint can even control ankle joint motion



Derofmity in Clubfoot

1.medial displacement of navicle and calcaneum around talus

2.talus forced into equinus by calcaneum and navicle wherease head and neck deviated medially .

3.calcaneus -inverted under talus with posterior end displaced upward and laterally and anterior end displaced downward and medially

3. 3D - it  appears varus .

4.soft tissue contractures or anomalies


 a.Talocalcaneal joint - opposed by 1.Calcaneofibular ligament 2. superior peroneal retinaculum 

                                                          3.posterior talocalcaneal ligament 4. superior peroneal

                                                            retinaculum

b. Talonavicular joint

                                  opposed by 1. Posterior Tibia ligament , 2. Deltoid ligament, 3.Spring ligament

                                                      4.Y-ligament           5.Talonavicular capsule

c. Calcaneocuboid ligament

                                 opposed by 1. long plantar ligament 2. plantar calcaneocuboid

If deformity persists late adaptive changes on bone  and some joints spontaneously fuse or go degenerative changes.

                                   



some terms at last

Deltoid ligament

                       tibial navicular

Spring ligament

                       calcaneonavicular ligament

Bifurcated Y ligament

                       calcaneonavicular oblique ligament.























































































                                                             















































































     


















Approach to a patient with Dwarfism

Young boy or a girl

height stunted

Ratio of upper and lower body height proportion normal or not (normally 1:1)

LE reaches upto middle thigh or down ?

proportion of arm and forearms looks normal

fingers shape is normal

lower extremity look shorter

alignment of LE on a photo shows multiplanar deformity of leg with anterior bowing and areas of flattening anateroposteriorly on leg

knee and hip are at flexion attitude ,

Intelligence - normal
Eye sight - normal

head ,neck examination - frontal bossing , sclera color , dentition , neck webbing ,

chest any signgs or deformity , belly protuded or not , umbilical hernia or not ,

back - kyphoscoliosis or not , dimpling of hair or not , any swellings on upper or lower extremities

gives  a clue to plan and proceed further





Impression

Rickets

Osteogenesis Imperfecta

   will have history of reccurent fractures with trivial trauma ,

    family history

    eyes color might be different , poor dentition


Polyostotic  Fibrous Dyslplasia

     dont have recurrent history of fracture ,

     leonine faces ,
 
      Mc Cune Albright Syndrome - precocious puberty and deformity


How to say deformity is on tibia ?

           does not correct with flexion of knee

 How to proceed ?

     Serum Calcium , Alkaline Phosphatase , Phosphorous Level

      Orthoscanogram

      Xray of affected parts

      Biopsy


Management ?

Coxa Vara and femoral medial bowing

 open multiple osteotomies

 William's technique of Multiple Osteotomies

   closed percutaneous osteotomy

  fixation ( rush nail / LC-DCP  in neutralization mode to prevent rotation )


same for bowing of tibia

Classification of Osteogenesis Imperfecta - very important .

 













   










Lumbar Spine - not to miss following points during examination

Contour

paraspinous muscles

 Errector Spinae or
 
 Sacrospinalis - Multifidus , Longissimus , Iliocostalis from medial to lateral

Symmetry

Pelvic Obliquity

Step off deformity

  Spondylolisthesis - body of involved vertebrae and rest of spine above slide forward

Lateral - Normal lordosis ,

                hyperlordosis - flexion contracture of hip

              flat back syndrome

                       compression fracture of lumbar vertebrae

               Gibbus - - sharp angular kyphosis kyphotic deformity

                              TB

Gait - antalgic

heel walk - 10 steps ,  L4 testing at L 3-4

toe walking

L5 - S1 testing

ROM - flexion 80- 90 , 10 cm to floor

extension 20 - 30 degrees

 lateral bending - 20 to 30 degrees

 rotation - 30 to 40 degrees

measurement - Schober test


Palpation

spinous process

counting L4-5 , level of iliac crest

paraspinous muscles - tender , tone

posterior facet joints

muscle testing

         flexion - rectus abdominis ,

           extension - errector spinae

Neurological

sensory

motor

 L1 and 2 - Iliopsoas

L 3 - Quadriceps ,

L4 - DF Ankle

L 5- EHL , Gluteus Medius , EDC

S1 - Peronei

       Gluetal Maximus

          Gastrosoleus

Reflexes - Normal patellar tendon reflexe , L 4

             L 5 - TP , Medial Hamstring

              S 1 - Achilles Tendon


Nerve Tension

   SLR

   Lasegue's test - DF after lowering 10 degrees from pain illicited during SLR

   Slump - variant of lasegue's test at sitting fom sitting looking straight ahead

                  allow C and T  vertebrae to collapse then bend head

               SLR and DF

                opposite side

             patient tells the experience

              thenn extend neck which relieves pain

 Bowstring sign - to point of repreoduction of pain , knee flexed

                            compress nerve on popliteal fossa

                            sensitivity 0.69 like lasegue's

Femoral Nerve Hyperextension test

Valsalva - Bearing down repoduces pain

Lumbar disc

 pain worsens with flexion

as opposed to spondylosis and spondylolisthesis

 no step off deformity



   

 

C-spine Examination - TB / Rhemuatoid Spondylitis not to miss following points

Look

skin  , vertebral alignment , dimpling, tuft of hair
Head , eyes , fact , neck , suprascapular/infrascapular region , hair level ,

Feel - Temperature, tenderness, spasm

Sensory Examination

upper limb  / upto c 8

power of muscles in upper extremities

Pulsation

Reflexes - Homan,s

                    spine - humeral

                   radial reflex

                   cross adduction thigh

                  clonus

Special test - Gait, Rhomberg test, Spurling ,Lhermitte test,  Distraction test , valsalva test

rule out problem of shoulder , brachial plexus and extra rib as they mimic the same sometimes.

functional like in torticollis


flow like from standing (front , sides and back ) , walking , squatting and sitting so as not to discomfort patients .

Torticollis - not to miss following points

Torticollis

Look
Anterior  - head position - centre or deviated to one side with rotation
                   decrease head and shoulder distance on one side 
                  facial aymmetry present or not ? 

                  eyes - nystagmus ?
        
                  taut sternocleidomastoid muscle
             
                   chest - muscles wasting present or not ? 


Side -          ear close or touching the shoulder

                   lordosis
        
                    comment on deltoid contour and elbow extended 

Back -
                    b/l shoulder symmetrical 
                    normal hairline 
                    scapula at same level 
                    occiput flat or nomal ? 

Gait / Squatting - Normal or not ? 

Feel - comment of taut sternocleidomastoid muscles, 
           palpate on sternum, clavicle , AC joint, Scapula and Proximal humerus 
           palpate on C-spine 

Movement 
         of Neck 
              Shoulder 
                

Neurology tests 
            Myotome 
            Dermatome 
            Reflexes 

cross adduction thigh
                                spine -humeral
                                reflex - radial
                                clonus
            Romber's Test - to quickly excluder any cord abnormality. 



  Vascular Examination of UE- Pulsation of Brachial , Radial and Ulnar Artery 

  

walking - normal squatting normal , romberg test negative

feel no tenderness

Sensory examination - normal UE




torticollis , hip disorder and club foot are considered a package disorder thatswhy when you find one try to exclude the presence of other during examination (that's the rational for checking squatting ).

C-spine affects all 4 extremities so also check reflexes on lower extremity. Gait and squatting  gives quick screening of motor power on lower extremity. Reflexes are tested separately.

Upper extremity requires a thorough test for sensory motor and reflexes in depth.






Club Foot Findings- Examination findings not to miss for this case

Look

Leg cylindrical

Dorsum - swelling on dorsolateral region lateral to ankle joint

skin - callosity

forefoot - adduction


toes alignment - normal

midfoot - cavus


lateal border convex

hindfoot varus

whole foot -shortened

foot wears - worn out

no torticollis , hip flexion normal

spin - no patch of hair , scoliosis and dimpling

feel - temperature normal ,
         no tenderness

 movement - active

 active

passive

deformity correctable or not

puslation - intact
sensation intact
motor power - muscles normal

reflexes - achillies tendon reflex , babinski's reflex

LLD , Lymph nodes










           

Sunday, 9 August 2020

Short Case - Cubitus Varus Deformity


Pratap Aryal  14 years  / boy   hospital no 017-1121000 , charikot , Nepal
C/O – Lt elbow deformity for 11 years

History of fall injury at the age of 3 years , and sustained injury around elbow . casted after 12 hours
for 3 weeks ( no documents to know the fractured part in elbow )
Deformity noticed which remained static .
No disabilities but he is not feeling well with the deformity
Personal History – He is a right hand dominant boy studying in class 8.

O/E
Introduction of ownself

Exposure upto Shoulder

Maintain privacy of the patient

Inspection

  Attitude of the Lt upper extremity

  Internally rotated
 Alignment  - cubitus varus deformity
Deformity is exaggerated in shoulder abduction
No wasting of muscles on arm forearm and hand
Normal overlying skin

Palpation
 Overlying temperature – normal
Skin texture – normal
No tenderness of soft tissue and bone
Lateral condyle , olecranon process and medial condyle at same line on extension and form isosceles triangle on flexion of 90 degrees
Movement
   Both active and passive
         Flexion 140 degrees
          Extension –  - 10 degrees
           Supination – 90 degrees
             Pronation  -- - 10 degrees

Measurement

  Cubitus varus deformity - -25 degrees

Distal Neurovasuclar test

 Sensation intact
 Motor intact
 Pulsation of radial / ulnar artert intact

Test hand if he can reach to perineum from back to show that left hand is required for perineal hygiene .



Impression – 14 years old boy with Lt Cuvitus Varus Deformity post  Supracondylar Fracture malunion  11 years back



VIVA

 What’s carrying angle ?
 Angle formed by long axis of arm to forearm .
Female – 14 degrees
Male 7- 10 degrees

Causes of Cubitus Varus deformity
 Malunited Supracondylar fracture
         BECASUSE of history of trauma
                                  No progressive deformity
                                  3 point bony relationship is maintained

How does cubitus varus deformity occur ?
Medial column collapse
IR , Anterior angulation contribute to this deformity.

Why extremity tends  to lie on IR attitude ?
So as to conceal the deformity.

How to treat this deformity ?
 Surgically
 Osteotomies
       Lateral closing Wedge Osteotomies , translation
       Medial Opening Wedge Osteotomy
                (    Donor site morbidity , graft dislodgement  and non union )
       Dome Osteotomy
       Step Cut osteotomy
        French Osteotomy
Classical one is Lateral closing wedge Osteotomy and fixation with TBW.

Complication of Cubitus Varus Deformity
   Elbow Instability
     Lateral condyle fracture
      Later Tardy Ulnar nerve Palsy